La maladie de Parkinson au Canada (serveur d'exploration)

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Bilateral Pallidal Stimulation for X-Linked Dystonia Parkinsonism

Identifieur interne : 001D38 ( Main/Exploration ); précédent : 001D37; suivant : 001D39

Bilateral Pallidal Stimulation for X-Linked Dystonia Parkinsonism

Auteurs : Pettarusp M. Wadia [Canada, Inde] ; Shen-Yang Lim [Canada, Malaisie] ; Andres M. Lozano [Canada] ; John R. Adams [Canada] ; Yu-Yan Poon [Canada] ; Cristina Torres Diaz [Canada] ; Elena Moro [Canada]

Source :

RBID : Pascal:10-0395121

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English descriptors

Abstract

Objective: To report the clinical benefits of bilateral deep brain stimulation (DBS) of the globus pallidus internus (GPi) in a patient with X-linked dystonia parkinsonism (XDP). Design: Case report. Setting: Tertiary referral center. Patient: A 40-year-old Filipino man with genetically confirmed XDP and severely disabling generalized dystonia. Intervention: Bilateral GPi DBS. Main Outcome Measures: The primary outcome measures were the Burke-Fahn-Marsden Dystonia Scale (BFMDS) severity and disability scores, and the secondary outcome measure was the Unified Parkinson Disease Rating Scores. Results: At the 1-year postoperative follow-up, there was 80.4% improvement in the BFMDS severity score and 66.7% improvement in the BFMDS disability score. Conclusion: Bilateral GPi DBS seems to be very effective in improving dystonia in XDP.


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Le document en format XML

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<div type="abstract" xml:lang="en">Objective: To report the clinical benefits of bilateral deep brain stimulation (DBS) of the globus pallidus internus (GPi) in a patient with X-linked dystonia parkinsonism (XDP). Design: Case report. Setting: Tertiary referral center. Patient: A 40-year-old Filipino man with genetically confirmed XDP and severely disabling generalized dystonia. Intervention: Bilateral GPi DBS. Main Outcome Measures: The primary outcome measures were the Burke-Fahn-Marsden Dystonia Scale (BFMDS) severity and disability scores, and the secondary outcome measure was the Unified Parkinson Disease Rating Scores. Results: At the 1-year postoperative follow-up, there was 80.4% improvement in the BFMDS severity score and 66.7% improvement in the BFMDS disability score. Conclusion: Bilateral GPi DBS seems to be very effective in improving dystonia in XDP.</div>
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